Primary Systemic Amyloidosis Questions & Answers

Updated: Aug 05, 2019
  • Author: Judit H Nyirady, MD, MBA; Chief Editor: Dirk M Elston, MD  more...
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Questions & Answers

Overview

What is primary systemic amyloidosis (PSA)?

What is the pathophysiology of primary systemic amyloidosis (PSA)?

What causes primary systemic amyloidosis (PSA)?

What is the prevalence of primary systemic amyloidosis (PSA) in the US?

What are the racial predilections of primary systemic amyloidosis (PSA)?

What are the sexual predilections of primary systemic amyloidosis (PSA)?

Which age group has the highest prevalence of primary systemic amyloidosis (PSA)?

What is the prognosis of primary systemic amyloidosis (PSA)?

Presentation

Which clinical history findings are characteristic in primary systemic amyloidosis (PSA)?

What are the signs and symptoms of primary systemic amyloidosis (PSA)?

Which physical findings are characteristic of primary systemic amyloidosis (PSA)?

What are the possible complications of primary systemic amyloidosis (PSA)?

DDX

Which conditions are included in the differential diagnoses of primary systemic amyloidosis (PSA)?

What are the differential diagnoses for Primary Systemic Amyloidosis?

Workup

What is the role of lab tests in the workup of primary systemic amyloidosis (PSA)?

What is the role of imaging studies in the workup of primary systemic amyloidosis (PSA)?

What is the role of biopsy in the workup of primary systemic amyloidosis (PSA)?

Which histologic findings are characteristic of primary systemic amyloidosis (PSA)?

Treatment

How is primary systemic amyloidosis (PSA) treated?

Medications

What is the role of medications in the treatment of primary systemic amyloidosis (PSA)?

Which medications in the drug class Immunomodulators are used in the treatment of Primary Systemic Amyloidosis?

Which medications in the drug class Uricosuric agents are used in the treatment of Primary Systemic Amyloidosis?

Which medications in the drug class Antineoplastic agents are used in the treatment of Primary Systemic Amyloidosis?

Which medications in the drug class Immunosuppressants are used in the treatment of Primary Systemic Amyloidosis?