Porphyria Cutanea Tarda Questions & Answers

Updated: Oct 19, 2020
  • Author: Anthony W Linfante, Jr, MD; Chief Editor: Dirk M Elston, MD  more...
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Questions & Answers

Overview

What is porphyria cutanea tarda?

What are causes porphyria cutanea tarda?

What is the pathophysiology of porphyria cutanea tarda?

What causes porphyria cutanea tarda?

What are risk factors for the development of porphyria cutanea tarda?

What is the prevalence of porphyria cutanea tarda in the US?

What is the global prevalence of porphyria cutanea tarda?

What is the racial predilection of porphyria cutanea tarda?

How does the prevalence of porphyria cutanea tarda vary by sex?

Which age groups have the highest prevalence of porphyria cutanea tarda?

What is the prognosis of porphyria cutanea tarda?

What is included in patient education for porphyria cutanea tarda?

Presentation

Which clinical history findings are characteristic of porphyria cutanea tarda?

Which physical findings are characteristic of porphyria cutanea tarda?

DDX

Which conditions should be included in the differential diagnoses of porphyria cutanea tarda?

What are the differential diagnoses for Porphyria Cutanea Tarda?

Workup

Which lab studies are performed in the workup of porphyria cutanea tarda?

What is the role of imaging studies in the workup of porphyria cutanea tarda?

How are hepatic fibrosis or cirrhosis assessed in the workup of porphyria cutanea tarda?

What is the role of biopsy in the workup of porphyria cutanea tarda?

Which histologic findings are characteristic of porphyria cutanea tarda?

Treatment

What is included in the treatment of porphyria cutanea tarda?

How is porphyria cutanea tarda managed during pregnancy?

What is the role of surgery in the management of porphyria cutanea tarda?

Which specialists should be consulted in the treatment of porphyria cutanea tarda?

Which dietary modifications are needed during treatment of porphyria cutanea tarda?

Which activity modification are used in the treatment of porphyria cutanea tarda?

What is included in the long-term monitoring of patients with porphyria cutanea tarda?

Medications

What is the role of medical therapy in the treatment of porphyria cutanea tarda?

Which medications in the drug class Bone Marrow Stimulants are used in the treatment of Porphyria Cutanea Tarda?

Which medications in the drug class Antimalarials are used in the treatment of Porphyria Cutanea Tarda?

Which medications in the drug class Chelators are used in the treatment of Porphyria Cutanea Tarda?