Medical Care
Tailor medical care to individual defects or functional impairment of the limbs or hearing.
Surgical Care
Surgical release of the constriction bands is used to preserve the digits (eg, Z-plasty, other methods for relaxing scars).
Consultations
Consultation with the following specialists may be needed:
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Surgeon - If any deformities of the fingers or craniofacial features are present
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Audiologist and speech therapist - If hearing loss is noted
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Other specialists - As indicated by clinical abnormalities
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Genetic counselor - Advisable to discuss risk of the offspring being affected by the syndrome
Diet
No dietary interventions are indicated for treatment. Oral bioavailability of retinoids is enhanced with food intake.
Activity
Activity is unrestricted.
Long-Term Monitoring
Regular follow-up by a dermatologist is recommended. Refer the patient to a surgeon if pseudoainhum develops. Further care and laboratory testing or radiography depend on the treatment selected, course, and complications. Audiologists and speech therapists may be referred on an individual basis.
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Starfish-shaped plaques.
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Palmar hyperkeratosis.
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Pseudoainhum.