Vohwinkel Syndrome Treatment & Management

Updated: Aug 13, 2019
  • Author: Zoltan Trizna, MD, PhD; Chief Editor: Dirk M Elston, MD  more...
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Treatment

Medical Care

Tailor medical care to individual defects or functional impairment of the limbs or hearing.

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Surgical Care

Surgical release of the constriction bands is used to preserve the digits (eg, Z-plasty, other methods for relaxing scars).

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Consultations

Consultation with the following specialists may be needed:

  • Surgeon - If any deformities of the fingers or craniofacial features are present

  • Audiologist and speech therapist - If hearing loss is noted

  • Other specialists - As indicated by clinical abnormalities

  • Genetic counselor - Advisable to discuss risk of the offspring being affected by the syndrome

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Diet

No dietary interventions are indicated for treatment. Oral bioavailability of retinoids is enhanced with food intake.

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Activity

Activity is unrestricted.

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Long-Term Monitoring

Regular follow-up by a dermatologist is recommended. Refer the patient to a surgeon if pseudoainhum develops. Further care and laboratory testing or radiography depend on the treatment selected, course, and complications. Audiologists and speech therapists may be referred on an individual basis.

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