Diagnostic Considerations
Also consider cerebriform intradermal nevus. [23, 25, 60]
People who are mentally retarded are a group of patients among whom the condition is very common. Cutis verticis gyrata is easily missed because it is usually covered with hair. Consider the diagnosis of Turner syndrome in female infants with cutis verticis gyrata with or without peripheral lymphedema. [61]
Missing the diagnosis (especially if it is due to a cerebriform intradermal nevus) may prove fatal if malignant transformation has occurred. [23, 24, 58, 62]
Differential Diagnoses
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Cutis verticis gyrata. Courtesy of DermNet New Zealand (http://www.dermnetnz.org/assets/Uploads/dermal-infiltrative/cvg2.jpg).
Tables
Malgorzata D Skibinska, MD, PhD Senior Lecturer, Department of Dermatology, Pediatric Dermatology and Oncology, Medical University of Łódź; Consultant Dermatologist and Allergist, Private Practice, Łódź, Poland
Malgorzata D Skibinska, MD, PhD is a member of the following medical societies: British Society of Allergy and Clinical Immunology, Polish Dermatological Society, Royal College of Physicians
Disclosure: Nothing to disclose.
Camila K Janniger, MD Clinical Professor of Dermatology, Clinical Associate Professor of Pediatrics, Chief of Pediatric Dermatology, Rutgers New Jersey Medical School
Camila K Janniger, MD is a member of the following medical societies: American Academy of Dermatology
Disclosure: Nothing to disclose.
David F Butler, MD Former Section Chief of Dermatology, Central Texas Veterans Healthcare System; Professor of Dermatology, Texas A&M University College of Medicine; Founding Chair, Department of Dermatology, Scott and White Clinic
David F Butler, MD is a member of the following medical societies: Alpha Omega Alpha, American Academy of Dermatology, Association of Military Dermatologists, Phi Beta Kappa, Texas Dermatological Society
Disclosure: Nothing to disclose.
Robert A Schwartz, MD, MPH Professor and Head of Dermatology, Professor of Pathology, Professor of Pediatrics, Professor of Medicine, Rutgers New Jersey Medical School
Robert A Schwartz, MD, MPH is a member of the following medical societies: Alpha Omega Alpha, American Academy of Dermatology, New York Academy of Medicine, Royal College of Physicians of Edinburgh, Sigma Xi, The Scientific Research Honor Society
Disclosure: Nothing to disclose.
Dirk M Elston, MD Professor and Chairman, Department of Dermatology and Dermatologic Surgery, Medical University of South Carolina College of Medicine
Dirk M Elston, MD is a member of the following medical societies: American Academy of Dermatology
Disclosure: Nothing to disclose.
Daniel J Hogan, MD Clinical Professor of Internal Medicine (Dermatology), Nova Southeastern University College of Osteopathic Medicine; Investigator, Hill Top Research, Florida Research Center
Daniel J Hogan, MD is a member of the following medical societies: Alpha Omega Alpha, American Academy of Dermatology, American Contact Dermatitis Society, Canadian Dermatology Association
Disclosure: Nothing to disclose.
