Epidermal Nevus Syndrome Questions & Answers

Updated: Apr 18, 2019
  • Author: Robert A Schwartz, MD, MPH; Chief Editor: William D James, MD  more...
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Questions & Answers

Overview

What is epidermal nevus syndrome (ENS)?

Which syndromes are associated with epidermal nevi (EN)?

What is the pathophysiology of epidermal nevus syndrome (ENS)?

What causes epidermal nevus syndrome (ENS)?

What is the prevalence of epidermal nevus syndrome (ENS)?

What are the sexual predilections of epidermal nevus syndrome (ENS)?

Which age groups have the highest prevalence of epidermal nevus syndrome (ENS)?

What is the prognosis of epidermal nevus syndrome (ENS)?

What is included in patient education about epidermal nevus syndrome (ENS)?

Presentation

Which clinical history findings are characteristic of epidermal nevus syndrome (ENS)?

Which physical findings are characteristic of linear nevus comedonicus?

Which physical findings are characteristic of inflammatory linear verrucous epidermal nevus (EN)?

Which physical findings are characteristic of linear sebaceous nevus (Jadassohn nevus phacomatosis)?

What are the possible complications of epidermal nevus syndrome (ENS)?

DDX

Which conditions are included in the differential diagnoses of epidermal nevus syndrome (ENS)?

What are the differential diagnoses for Epidermal Nevus Syndrome?

Workup

What is the role of imaging studies in the workup of epidermal nevus syndrome (ENS)?

What is the role of EEG in the diagnosis of epidermal nevus syndrome (ENS)?

Which histologic findings are characteristic of epidermal nevus syndrome (ENS)?

Treatment

How is epidermal nevus syndrome (ENS) treated?

What is the role of surgery in the treatment of epidermal nevus syndrome (ENS)?

Which specialist consultations are beneficial to patients with epidermal nevus syndrome (ENS)?

How is epidermal nevus syndrome (ENS) prevented?

Medications

What is the role of medications in the treatment of epidermal nevus syndrome (ENS)?

Which medications in the drug class Vitamin D analogues are used in the treatment of Epidermal Nevus Syndrome?