Surgical Care

Surgical excision of the dermal lesions is indicated only for cosmetic reasons. In some patients, surgical treatment of deafness is possible. Surgical treatment of associated conditions, such as stenosis of the aortae, should be performed as appropriate.

Consultations

Note the following potential consultations:

Laryngologic examination with audiogram
Ophthalmologic examination with ophthalmoscopy
General physical examination with ECG

Activity

Osteopoikilosis is asymptomatic; however, 15-20% of patients experience pain and joint effusions. Usually, no special restrictions in activity are required.^[5]

Long-Term Monitoring

There are no specific follow-up requirements in the case of asymptomatic dermatofibrosis lenticularis (Buschke-Ollendorff syndrome).

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Media Gallery

Plaque of grouped papular eruptions on the thigh.
Hematoxylin and eosin stain shows the histopathologic features of the skin lesions.
Small longitudinal lesions of increased bone density in the proximal epiphysis of the left tibial bone and in the distal epiphysis of the right tibial bone.
Orcein stain of elastic fibers shows the histopathologic features of the skin lesions.
Weigert stain of the elastic fibers shows the histopathologic features of the skin lesions.
Plaque of grouped papules on the abdominal coat.

of 6

Author

Vernon J Forrester, MD Fellow, Cleveland Clinic

Disclosure: Nothing to disclose.

Coauthor(s)

Krista Roncone University of Virginia School of Medicine

Disclosure: Nothing to disclose.

Barbara B Wilson, MD Edward P Cawley Associate Professor, Department of Dermatology, University of Virginia School of Medicine

Barbara B Wilson, MD is a member of the following medical societies: Alpha Omega Alpha, American Academy of Dermatology, Medical Society of Virginia, Sigma Xi, The Scientific Research Honor Society

Disclosure: Nothing to disclose.

Specialty Editor Board

David F Butler, MD Former Section Chief of Dermatology, Central Texas Veterans Healthcare System; Professor of Dermatology, Texas A&M University College of Medicine; Founding Chair, Department of Dermatology, Scott and White Clinic

David F Butler, MD is a member of the following medical societies: Alpha Omega Alpha, American Academy of Dermatology, Association of Military Dermatologists, Phi Beta Kappa, Texas Dermatological Society

Disclosure: Nothing to disclose.

Robert A Schwartz, MD, MPH Professor and Head of Dermatology, Professor of Pathology, Professor of Pediatrics, Professor of Medicine, Rutgers New Jersey Medical School

Robert A Schwartz, MD, MPH is a member of the following medical societies: Alpha Omega Alpha, American Academy of Dermatology, New York Academy of Medicine, Royal College of Physicians of Edinburgh, Sigma Xi, The Scientific Research Honor Society

Disclosure: Nothing to disclose.

Chief Editor

Dirk M Elston, MD Professor and Chairman, Department of Dermatology and Dermatologic Surgery, Medical University of South Carolina College of Medicine

Dirk M Elston, MD is a member of the following medical societies: American Academy of Dermatology

Disclosure: Nothing to disclose.

Additional Contributors

Jacek C Szepietowski, MD, PhD Professor, Vice-Head, Department of Dermatology, Venereology and Allergology, Wroclaw Medical University; Director of the Institute of Immunology and Experimental Therapy, Polish Academy of Sciences, Poland

Disclosure: Received consulting fee from Orfagen for consulting; Received consulting fee from Maruho for consulting; Received consulting fee from Astellas for consulting; Received consulting fee from Abbott for consulting; Received consulting fee from Leo Pharma for consulting; Received consulting fee from Biogenoma for consulting; Received honoraria from Janssen for speaking and teaching; Received honoraria from Medac for speaking and teaching; Received consulting fee from Dignity Sciences for consulting; .

Grazyna Szybejko-Machaj, MD, PhD Assistant Professor, Department of Dermatology, Wroclaw Medical University

Disclosure: Nothing to disclose.

Lukasz Matusiak, MD, PhD Assistant, Department and Clinic of Dermatology, Venereology and Allergology, Medical University of Wroclaw

Disclosure: Nothing to disclose.

Acknowledgements

Mark A Crowe, MD Assistant Clinical Instructor, Department of Medicine, Division of Dermatology, University of Washington School of Medicine

Mark A Crowe, MD is a member of the following medical societies: American Academy of Dermatology and North American Clinical Dermatologic Society

Disclosure: Nothing to disclose.

Mieczyslawa Miklaszewska, MD, PhD Professor, Department of Dermatology, Medical University in Wroclaw, Poland

Disclosure: Nothing to disclose.

Sections Dermatofibrosis Lenticularis (Buschke-Ollendorf Syndrome)
Overview
Presentation
DDx
Workup
Treatment
Media Gallery
References

Dermatofibrosis Lenticularis (Buschke-Ollendorf Syndrome) Treatment & Management

Surgical Care

Consultations

Activity

Long-Term Monitoring

References

Tables

Contributor Information and Disclosures

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