Hermansky-Pudlak Syndrome Medication

Updated: Dec 11, 2019
  • Author: Natalio J Izquierdo, MD; Chief Editor: Hampton Roy, Sr, MD  more...
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Medication

Medication Summary

Several medications have been used to try to diminish bleeding diathesis in patients with Hermansky-Pudlak syndrome (HPS).

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Hemostatic agents

Class Summary

Are potent inhibitors of fibrinolysis and can reverse states that are associated with excessive fibrinolysis.

Desmopressin

A synthetic analogue of the natural pituitary hormone 8-arginine vasopressin (ADH), an antidiuretic hormone affecting renal water conservation. Indicated for patients with hemophilia A and mild von Willebrand disease to maintain hemostasis. If used preoperatively, administer 30 min prior to scheduled procedure.

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