Ebstein Anomaly Differential Diagnoses

Updated: Jun 14, 2023
  • Author: Kamran Riaz, MD; Chief Editor: Yasmine S Ali, MD, MSCI, FACC, FACP  more...
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Diagnostic Considerations

Ebstein anomaly should not be confused with Uhl anomaly, a congenital heart disease characterized by a hypoplastic, underdeveloped inflow segment of the right ventricle with tricuspid leaflets arising appropriately from the annulus.

Rule out Ebstein anomaly in patients with the following:

  • Accessory pathway-mediated Wolff-Parkinson-White (WPW) syndrome and supraventricular tachycardia (SVT)

  • Cyanotic congenital heart diseases

  • Atrial septal defect (ASD)

  • Cases of severe right heart failure

  • Isolated severe tricuspid regurgitation

  • L-transposition of the great vessels

Differential Diagnoses