Ebstein Anomaly Differential Diagnoses

Updated: Jan 17, 2017
  • Author: Kamran Riaz, MD; Chief Editor: Yasmine Subhi Ali, MD, FACC, FACP, MSCI  more...
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DDx

Diagnostic Considerations

Ebstein anomaly should not be confused with Uhl anomaly, a congenital heart disease characterized by a hypoplastic, underdeveloped inflow segment of the right ventricle with tricuspid leaflets arising appropriately from the annulus.

Rule out Ebstein anomaly in patients with the following:

  • Accessory pathway-mediated Wolff-Parkinson-White (WPW) syndrome and supraventricular tachycardia (SVT)
  • Cyanotic congenital heart diseases
  • Atrial septal defect (ASD)
  • Cases of severe right heart failure
  • Isolated severe tricuspid regurgitation
  • L-transposition of the great vessels

Differential Diagnoses