Chester Porphyria Treatment & Management

Updated: Aug 07, 2020
  • Author: Danielle Nance, MD; Chief Editor: Emmanuel C Besa, MD  more...
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Treatment

Approach Considerations

Currently, no cure exists for Chester porphyria. The goal of management is to avoid precipitating factors in cases of suspected porphyrias. Treatment is symptomatic and includes supportive care with IV fluids and pain management. Treatments that are known to be effective in acute intermittent porphyria and variegate porphyria are expected to benefit patients with Chester prophyria. Genetic counseling and understanding the disease and its manifestations may be helpful for family members.

Patients with Chester porphyria are at risk of an acute attack of porphyria at the time of surgery. This is because of stress, metabolic abnormalities, and certain drugs used during surgery.

Eating a balanced diet is important in maintaining health for patients with chronic medical conditions. Nutritional counseling can assist in identifying triggers and potential dietary support to prevent attacks, and maintain weight during an attack. 

Regular activity to maintain health is an important part of the management of Chester porphryia.