Interstitial (Nonidiopathic) Pulmonary Fibrosis Questions & Answers

Updated: Oct 16, 2018
  • Author: Eleanor M Summerhill, MD, FACP, FCCP; Chief Editor: Zab Mosenifar, MD, FACP, FCCP  more...
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Questions & Answers

Overview

What are diffuse parenchymal lung diseases (DPLDs)?

What is the pathophysiology of diffuse parenchymal lung diseases (DPLDs)?

Which diffuse parenchymal lung diseases (DPLDs) are associated with rheumatologic/connective-tissue diseases?

Which diffuse parenchymal lung diseases (DPLDs) are associated with drug exposure?

Which diffuse parenchymal lung diseases (DPLDs) mimic interstitial lung disease?

Which diffuse parenchymal lung diseases (DPLDs) are associated with environmental or occupational exposures?

Which diffuse parenchymal lung diseases (DPLDs) are associated with systemic illnesses?

What is the incidence of diffuse parenchymal lung diseases (DPLDs) in the US?

What is the global incidence of diffuse parenchymal lung diseases (DPLDs)?

What are the racial predilections of diffuse parenchymal lung diseases (DPLDs)?

How does the incidence of diffuse parenchymal lung diseases (DPLDs) vary by sex?

How does the incidence of diffuse parenchymal lung diseases (DPLDs) vary by age?

What is the prognosis of diffuse parenchymal lung diseases (DPLDs)?

What information about diffuse parenchymal lung diseases (DPLDs) should patients be given?

Presentation

Which clinical history findings are characteristic of diffuse parenchymal lung diseases (DPLDs)?

How are diffuse parenchymal lung diseases (DPLDs) diagnosed?

How are manifestations of diffuse parenchymal lung diseases (DPLDs) categorized?

Which diffuse parenchymal lung diseases (DPLDs) are characterized as chronic, insidious, and slowly progressive?

Which diffuse parenchymal lung diseases (DPLDs) are characterized as subacute?

Which diffuse parenchymal lung diseases (DPLDs) are characterized as acute onset?

Which physical findings are characteristic of diffuse parenchymal lung diseases (DPLDs)?

What are the disease-specific findings of diffuse parenchymal lung diseases (DPLDs)?

What are the potential complications of diffuse parenchymal lung diseases (DPLDs)?

DDX

What are the differential diagnoses for Interstitial (Nonidiopathic) Pulmonary Fibrosis?

Workup

What is the role of lab studies in the diagnosis of diffuse parenchymal lung diseases (DPLDs)?

What is the role of imaging studies in the diagnosis of diffuse parenchymal lung diseases (DPLDs)?

Which findings seen on high-resolution chest CT scanning suggest diffuse parenchymal lung diseases (DPLDs)?

What is the role of pulmonary function testing in the diagnosis of diffuse parenchymal lung diseases (DPLDs)?

What is the role of arterial blood gas analysis in the diagnosis of diffuse parenchymal lung diseases (DPLDs)?

What is the role of pulmonary exercise testing in the diagnosis of diffuse parenchymal lung diseases (DPLDs)?

Which procedures are performed in the diagnosis of diffuse parenchymal lung diseases (DPLDs)?

Which histologic findings are characteristic of diffuse parenchymal lung diseases (DPLDs)?

What are prognostic indicators for diffuse parenchymal lung diseases (DPLDs) staged?

Treatment

What is included in general supportive care for diffuse parenchymal lung diseases (DPLDs)?

What is the role of pharmacologic therapy in the treatment of diffuse parenchymal lung diseases (DPLDs)?

What is the role of surgery in the treatment of diffuse parenchymal lung diseases (DPLDs)?

Which specialist consultations are beneficial for patients with diffuse parenchymal lung diseases (DPLDs)?

Which dietary modifications are beneficial in the treatment of diffuse parenchymal lung diseases (DPLDs)?

Which activity modifications are beneficial in the treatment of diffuse parenchymal lung diseases (DPLDs)?

What should be included in the long-term monitoring of diffuse parenchymal lung diseases (DPLDs)?

Medications

Which medications are used in the treatment of diffuse parenchymal lung diseases (DPLDs)?

Which medications in the drug class Transforming Growth Factor Inhibitors are used in the treatment of Interstitial (Nonidiopathic) Pulmonary Fibrosis?

Which medications in the drug class Pulmonary, Tyrosine Kinase Inhibitors are used in the treatment of Interstitial (Nonidiopathic) Pulmonary Fibrosis?

Which medications in the drug class Anti-inflammatories are used in the treatment of Interstitial (Nonidiopathic) Pulmonary Fibrosis?

Which medications in the drug class Immunosuppressants are used in the treatment of Interstitial (Nonidiopathic) Pulmonary Fibrosis?

Which medications in the drug class Corticosteroids are used in the treatment of Interstitial (Nonidiopathic) Pulmonary Fibrosis?