Restrictive Lung Disease Questions & Answers

Updated: Sep 16, 2020
  • Author: Jonathan Robert Caronia, DO; Chief Editor: John J Oppenheimer, MD  more...
  • Print
Questions & Answers

Overview

How is restrictive lung disease characterized?

How is the mnemonic PAINT used to divide the causes of restrictive lung disease?

What is the pathophysiology of restrictive lung disease?

Which intrinsic lung diseases have an etiologic role in restrictive lung disease?

Which idiopathic fibrotic disorders have a role in the etiology of restrictive lung disease?

Which extrinsic disorders have a role in the etiology of restrictive lung disease?

What is the prevalence of restrictive lung disease in the US?

What is the global prevalence of restrictive lung disease?

What are the racial predilections of restrictive lung disease?

How does the prevalence of restrictive lung disease vary by sex?

Which age groups are at highest risk for restrictive lung disease?

What is the prognosis of restrictive lung disease?

What is the mortality and morbidity associated with restrictive lung disease?

Presentation

What should be the focus of patient history in the evaluation of restrictive lung disease?

Why is illness duration significant in the history of restrictive lung disease?

What is the importance of smoking history in restrictive lung disease?

What is the importance of prior medication use in the history of restrictive lung disease?

Which family history may be related to restrictive lung disease?

Which occupational history may be related to restrictive lung disease?

What is the importance of environmental exposure history in the evaluation of restrictive lung disease?

What are the signs and symptoms of intrinsic disorder caused restrictive lung disease?

What are the signs and symptoms of extrinsic disorder caused restrictive lung disease?

Which physical findings are characteristic of intrinsic disorders causing restrictive lung disease?

Which physical findings are characteristic of restrictive lung disease due to extrinsic disorders?

What are the complications of restrictive lung disease?

DDX

What are the differential diagnoses for Restrictive Lung Disease?

Workup

What is the role of lab studies in the evaluation of intrinsic lung disease causes of restrictive lung disease?

What is the role of lab studies in the evaluation of extrinsic lung disease causes of restrictive lung disease?

What is the role of chest radiography in the evaluation of intrinsic lung disorder causes for restrictive lung disease?

What is the role of chest CT in the evaluation of restrictive lung disease?

What is the role of lung ultrasonography in the evaluation for restrictive lung disease?

What is the role of imaging studies in the evaluation of extrinsic disorder causes of restrictive lung disease?

What is the role of pulmonary function testing in the evaluation of restrictive lung disease?

Which tests may be performed in the evaluation of extrinsic lung disorder causes of restrictive lung disease?

What is the role of bronchoalveolar lavage in the workup of restrictive lung disease?

What is the role of lung biopsy in the workup of restrictive lung disease?

What is the role of video-assisted thoracoscopic lung biopsy in the workup of restrictive lung disease?

Which histological findings are characteristic of restrictive lung disease?

Treatment

What are the treatment options for restrictive lung disease?

What are the treatment options for idiopathic pulmonary fibrosis in restrictive lung disease?

What is the role of corticosteroids in the treatment of restrictive lung disease?

What is the role of cytotoxic therapy in the treatment of restrictive lung disease?

What is the role of antifibrotic therapies in the treatment of restrictive lung disease?

How are collagen-vascular diseases managed in restrictive lung disease?

How is sarcoidosis treated in restrictive lung disease?

How are extrinsic lung disorders treated in restrictive lung disease?

When is surgical intervention indicated for restrictive lung disease?

Which specialist consultations may be beneficial in the treatment of restrictive lung disease?

How are acute exacerbations managed in restrictive lung disease?

Medications

Which medications are used in the treatment of restrictive lung disease?

Which medications in the drug class Pulmonary, Tyrosine Kinase Inhibitors are used in the treatment of Restrictive Lung Disease?

Which medications in the drug class Anti-inflammatory agents are used in the treatment of Restrictive Lung Disease?

Which medications in the drug class Cytotoxic agents are used in the treatment of Restrictive Lung Disease?

Which medications in the drug class Corticosteroids are used in the treatment of Restrictive Lung Disease?