Pediatric Wiskott-Aldrich Syndrome Follow-up

Updated: Jun 12, 2020
  • Author: Robert A Schwartz, MD, MPH; Chief Editor: Harumi Jyonouchi, MD  more...
  • Print
Follow-up

Further Inpatient Care

In general, admit a patient with Wiskott-Aldrich syndrome (WAS) with bleeding or pulmonary infection because the extent of bleeding may be difficult to ascertain or bleeding may be difficult to control.

Similarly, infections such as pneumonia may be accompanied by sepsis or require respiratory support; inpatient management is usually wise.

The patient's risk for bleeding and the presence of any chronic illness complicate diagnosis and treatment of malignancies.

Next:

Transfer

Because any primary immunodeficiency disease is associated with a great complexity of medical problems, most clinical immunologists strongly think an immunologist should manage these patients. High early mortality rates and a high rate of complications in Wiskott-Aldrich syndrome suggest frequent monitoring by a clinical immunologist is essential.

Transfers are most likely to a bone marrow transplantation unit for stem cell reconstitution. These units customarily provide social services and psychological support for the patient and family in addition to the requisite medical care.

Previous