Differential Diagnoses

Workup

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Media Gallery

Subcostal echocardiographic view of a child with a secundum atrial septal defect (ASD). Note the position of the defect in the atrial septum. LA = left atrium; RA = right atrium; SVC = superior vena cava.
Subcostal long-axis view of the same child as in the previous image with a secundum atrial septal defect (ASD). LA = left atrium; RA = right atrium; RUPV = right upper pulmonary vein.
Parasternal short axis view of a child with a secundum atrial septal defect (ASD). AO = aorta; LA = left atrium; RA = right atrium.
Apical echocardiographic view of a primum atrial septal defect (ASD). Note the position of the defect when compared with a secundum ASD. LA = left atrium; LV = left ventricle; RA = right atrium; RV = right ventricle.
Apical echocardiographic view of a primum atrial septal defect (ASD). Note that the atrioventricular valves are at the same level (instead of mild apical displacement of the tricuspid valve), which is seen in the spectrum of atrioventricular canal defects. LA = left atrium; LV = left ventricle; RA = right atrium; RV = right ventricle.
Apical color Doppler echocardiographic view of a primum atrial septal defect (ASD). Note the flow across the defect from the left atrium to the right atrium (RA), and note the mitral regurgitation (MR) through a cleft in the anterior leaflet of the mitral valve. LV = left ventricle; MV = mitral valve.
Subcostal short-axis view of a child with a sinus venosus atrial septal defect (ASD). Note the position of the defect compared with that of a secundum or primum ASD. Also note the anomalous position of the right upper pulmonary vein (RUPV). LA = left atrium; RA = right atrium.
Electrocardiographs (ECGs) from a child with a secundum atrial septal defect (ASD). Note the right-axis deviation and rSR' pattern in lead V1.
Electrocardiogram (ECG) from a child with a primum atrial septal defect (ASD). Note the left-axis deviation with a counterclockwise vector of depolarization (small q waves in leads I and aVL) and right ventricular hypertrophy and/or volume overload (rSR' pattern and upright T wave in lead V1).

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Author

Michael R Carr, MD Pediatric Cardiologist, Assistant Professor of Pediatrics, Northwestern University Feinberg School of Medicine

Michael R Carr, MD is a member of the following medical societies: Alpha Omega Alpha, American Academy of Pediatrics, American College of Cardiology, American Heart Association, American Society of Echocardiography

Disclosure: Nothing to disclose.

Coauthor(s)

Brent R King, MD, MMM Clive, Nancy, and Pierce Runnells Distinguished Professor of Emergency Medicine, Professor of Pediatrics, University of Texas Health Science Center at Houston; Chair, Department of Emergency Medicine, Chief of Emergency Services, Memorial Hermann Hospital and LBJ Hospital

Brent R King, MD, MMM is a member of the following medical societies: American Academy of Emergency Medicine, American Academy of Pediatrics, American College of Emergency Physicians, American Association for Physician Leadership, Society for Academic Emergency Medicine

Disclosure: Nothing to disclose.

Specialty Editor Board

Mary L Windle, PharmD Adjunct Associate Professor, University of Nebraska Medical Center College of Pharmacy; Editor-in-Chief, Medscape Drug Reference

Disclosure: Nothing to disclose.

Alvin J Chin, MD Emeritus Professor of Pediatrics, University of Pennsylvania School of Medicine

Disclosure: Nothing to disclose.

Chief Editor

Syamasundar Rao Patnana, MD Professor of Pediatrics and Medicine, Division of Cardiology, Emeritus Chief of Pediatric Cardiology, University of Texas Medical School at Houston and Children's Memorial Hermann Hospital

Syamasundar Rao Patnana, MD is a member of the following medical societies: American Academy of Pediatrics, American Pediatric Society, American College of Cardiology, American Heart Association, Society for Cardiovascular Angiography and Interventions, Society for Pediatric Research

Disclosure: Nothing to disclose.

Additional Contributors

Paul M Seib, MD Associate Professor of Pediatrics, University of Arkansas for Medical Sciences; Medical Director, Cardiac Catheterization Laboratory, Co-Medical Director, Cardiovascular Intensive Care Unit, Arkansas Children's Hospital

Paul M Seib, MD is a member of the following medical societies: American Academy of Pediatrics, American College of Cardiology, American Heart Association, Arkansas Medical Society, International Society for Heart and Lung Transplantation, Society for Cardiovascular Angiography and Interventions

Disclosure: Nothing to disclose.

Sections Pediatric Atrial Septal Defects
Overview
Presentation
DDx
Workup
Treatment
Media Gallery
References

Pediatric Atrial Septal Defects Differential Diagnoses

Differential Diagnoses

References

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