DDx
Diagnostic Considerations
Important considerations
It is important for clinicians to recognize double-chambered right ventricle (DCRV) in the presence of associated defects, particularly ventricular septal defect (VSD), which may result in reoperation.
Rule out residual lesions.
Provide follow-up care for patients with recurrent right ventricle obstruction.
Special concerns
Once the associated lesions have been repaired and the abnormal muscle bundles have been resected, pregnancy carries no additional risks. The same applies if mild gradients across the right ventricular outflow tract exist.
Other problems to be considered
Also consider the possibility of a foreign body simulating a double-chambered right ventricle (one case report).
Differential Diagnoses
Media Gallery
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Double-Chambered Right Ventricle. Electrocardiogram of an 18-month-old boy with double-chambered right ventricle. Note the upright T waves in the right precordial leads.
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Double-Chambered Right Ventricle. Right anterior oblique (RAO) angiogram demonstrating proximal and distal chambers of right ventricle (Image courtesy of R.M. Freedom, MD).
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Double-Chambered Right Ventricle. Lateral right ventriculography of a patient with double-chambered right ventricle. Large arrow indicates the presence of a fibromuscular obstruction with division of the right ventricle; small arrows outline pulmonary valve stenosis (Image courtesy of R.M. Freedom, MD).
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Double-Chambered Right Ventricle. Subcostal right anterior oblique (RAO) echocardiograph view demonstrating right ventricle muscle bundles separating proximal from distal (*) chamber. PV = Pulmonary valve (Image courtesy of J. Smallhorn, MD)
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Double-Chambered Right Ventricle. Subcostal right anterior oblique (RAO) echocardiograph view with color Doppler demonstrating ventricular septal defect jet to proximal chamber. (*) = Distal chamber (Image courtesy of J. Smallhorn, MD).
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