Medication Summary

Drug therapy is not currently a component of the standard of care for double-chambered right ventricle (DCRV). See Treatment.

In the presence of a ventricular septal defect with a significant left to right shunt, diuretics and other antifailure measures may be required.

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Media Gallery

Double-Chambered Right Ventricle. Electrocardiogram of an 18-month-old boy with double-chambered right ventricle. Note the upright T waves in the right precordial leads.
Double-Chambered Right Ventricle. Right anterior oblique (RAO) angiogram demonstrating proximal and distal chambers of right ventricle (Image courtesy of R.M. Freedom, MD).
Double-Chambered Right Ventricle. Lateral right ventriculography of a patient with double-chambered right ventricle. Large arrow indicates the presence of a fibromuscular obstruction with division of the right ventricle; small arrows outline pulmonary valve stenosis (Image courtesy of R.M. Freedom, MD).
Double-Chambered Right Ventricle. Subcostal right anterior oblique (RAO) echocardiograph view demonstrating right ventricle muscle bundles separating proximal from distal (*) chamber. PV = Pulmonary valve (Image courtesy of J. Smallhorn, MD)
Double-Chambered Right Ventricle. Subcostal right anterior oblique (RAO) echocardiograph view with color Doppler demonstrating ventricular septal defect jet to proximal chamber. (*) = Distal chamber (Image courtesy of J. Smallhorn, MD).

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Author

Shubhayan Sanatani, MD, FRCPC, FHRS Head, Division of Cardiology, Professor, Department of Pediatrics, University of British Columbia Faculty of Medicine; Medical Director, Children's Heart Centre, Section Head, Heart Rhythm Service, British Columbia Children's Hospital, Canada

Shubhayan Sanatani, MD, FRCPC, FHRS is a member of the following medical societies: British Columbia Medical Association, Canadian Cardiovascular Society, Canadian Heart Rhythm Society, Canadian Medical Association, Royal College of Physicians and Surgeons of Canada

Disclosure: Serve(d) as a director, officer, partner, employee, advisor, consultant or trustee for: Emtelligent<br/>Received research grant from: Heart and Stroke Foundation of Canada.

Specialty Editor Board

Mary L Windle, PharmD Adjunct Associate Professor, University of Nebraska Medical Center College of Pharmacy; Editor-in-Chief, Medscape Drug Reference

Disclosure: Nothing to disclose.

Julian M Stewart, MD, PhD Associate Chairman of Pediatrics, Director, Center for Hypotension, Westchester Medical Center; Professor of Pediatrics and Physiology, New York Medical College

Julian M Stewart, MD, PhD is a member of the following medical societies: American Academy of Pediatrics, American Autonomic Society, American Physiological Society

Disclosure: Received research grant from: Lundbeck Pharmaceuticals<br/>Received grant/research funds from Lundbeck Pharmaceuticals for none.

Chief Editor

Stuart Berger, MD Executive Director of The Heart Center, Interim Division Chief of Pediatric Cardiology, Lurie Childrens Hospital; Professor, Department of Pediatrics, Northwestern University, The Feinberg School of Medicine

Stuart Berger, MD is a member of the following medical societies: American Academy of Pediatrics, American College of Cardiology, American College of Chest Physicians, American Heart Association, Society for Cardiovascular Angiography and Interventions

Disclosure: Nothing to disclose.

Acknowledgements

Alejandro R Peirone, MD Head, Section of Pediatric Cardiology, Hospital Privado de Cordoba; Consulting Staff, Division of Pediatric Cardiology, Hospital Espanol Medical Plaza and Children's Hospital of Cordoba

Disclosure: Nothing to disclose.

Sections Double-Chambered Right Ventricle
Overview
Presentation
DDx
Workup
Treatment
Medication
Media Gallery
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Double-Chambered Right Ventricle Medication

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