Pediatric Biliary Atresia Questions & Answers

Updated: May 03, 2019
  • Author: Steven M Schwarz, MD, FAAP, FACN, AGAF; Chief Editor: Carmen Cuffari, MD  more...
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Questions & Answers

Overview

What is pediatric biliary atresia?

What is the pathophysiology of pediatric biliary atresia?

What is the prevalence of pediatric biliary atresia in the US?

What is the global prevalence of pediatric biliary atresia?

What is the mortality and morbidity associated with pediatric biliary atresia?

What are the racial predilections of pediatric biliary atresia?

What are the sexual predilections of pediatric biliary atresia?

At what age is pediatric biliary atresia typically diagnosed?

Presentation

Which clinical history findings are characteristic of pediatric biliary atresia?

Which physical findings are characteristic of pediatric biliary atresia?

What causes pediatric biliary atresia?

What are the infectious causes of pediatric biliary atresia?

What is the role of genetics in the etiology of pediatric biliary atresia?

What is the role of bile acids in the etiology of pediatric biliary atresia?

What are the immunological causes of pediatric biliary atresia?

DDX

What are the differential diagnoses for Pediatric Biliary Atresia?

Workup

What is the role of serum bilirubin measurement in the workup of pediatric biliary atresia?

What is the role of a liver function panel in the workup of pediatric biliary atresia?

What is the role of serum alpha1-antitrypsin with Pi typing in the workup of pediatric biliary atresia?

How is cystic fibrosis diagnosed in the evaluation of pediatric biliary atresia?

What is the role of ultrasonography in the workup of pediatric biliary atresia?

What is the role of hepatobiliary scintiscanning the workup of pediatric biliary atresia?

How is duodenal bile excretion assessed in the workup of pediatric biliary atresia?

What is the role of ERCP in the workup of pediatric biliary atresia?

What is the role of liver biopsy in the workup of pediatric biliary atresia?

What is the role of e cholangiography in the workup of pediatric biliary atresia?

Which histologic findings are characteristic of pediatric biliary atresia?

Treatment

How is pediatric biliary atresia treated?

What is the role of surgery in the treatment of pediatric biliary atresia?

Which specialist consultations are beneficial to patients with pediatric biliary atresia?

Which dietary modifications are used in the treatment of pediatric biliary atresia?

What is included in the long-term monitoring of pediatric biliary atresia?

Medications

What is the role of medications in the treatment of pediatric biliary atresia?

Which medications in the drug class Antibiotics are used in the treatment of Pediatric Biliary Atresia?

Which medications in the drug class Bile acids are used in the treatment of Pediatric Biliary Atresia?

Follow-up

What is the role of steroid therapy in the treatment of pediatric biliary atresia?

What are the possible complications of pediatric biliary atresia?

What is the prognosis of pediatric biliary atresia?