Roberts EA. Primary sclerosing cholangitis in children. J Gastroenterol Hepatol. 1999 Jun. 14(6):588-93. [Medline].
Ludwig J. Small-duct primary sclerosing cholangitis. Semin Liver Dis. 1991. 11:11-17. [Medline].
Rodriguez HJ Bss NM. Primary Sclerosing Cholangitis. Semin Gastrointest Dis. 2003. 14:189-98. [Medline].
MacFaul GR, Chapman RW. Sclerosing cholangitis. Curr opin gastroenterol. 2004. 20:275-990. [Medline].
Hyams J., Markowitz J., Treem W., et al. Characterization of hepatic abnormalities in children with inflammatory bowel disease. Inflamm Bowel Dis. 1995. 1:27-33. [Medline].
Aron JH, Bowlus CL. The immunobiology of primary sclerosing cholangitis. Semin Immunopathol. 2009 May 26. [Medline].
Aoki CA, Bowlus CL, Gershwin ME. The immunobiology of primary sclerosing cholangitis. Autoimmun Rev. 2005 Mar. 4(3):137-43. [Medline].
Narayanan Menon KV, Wiesner RH. Etiology and natural history of primary sclerosing cholangitis. J Hepatobiliary Pancreat Surg. 1999. 6(4):343-51. [Medline].
Girard M, Franchi-Abella S, Lacaille F, Debray D. Specificities of sclerosing cholangitis in childhood. Clinics and Research in Hepatology and Gastroenteorlogy. 2012. 36:530-35. [Medline].
Worthington J, Cullen S, Chapman R. Immunopathogenesis of primary sclerosing cholangitis. Clin Rev Allergy Immunol. 2005. 28:93-103. [Medline].
Pall H, Zielenski J, Jonas MM, DaSilva DA, Potvin KM, Yuan XW, et al. Primary sclerosing cholangitis in childhood is associated with abnormalities in cystic fibrosis-mediated chloride channel function. J Pediatr. 2007 Sep. 151(3):255-9. [Medline].
Feld JJ, Heathcote EJ. Epidemiology of autoimmune liver disease. J Gastroenterol Hepatol. 2003 Oct. 18(10):1118-28. [Medline].
Feldstein AE, Perrault J, El-Youssif M, et al. Primary sclerosing cholangitis in children: a long-term follow-up study. Hepatology. 2003 Jul. 38(1):210-7. [Medline].
Sisto A, Feldman P, Garel L, et al. Primary sclerosing cholangitis in children: study of five cases and review of the literature. Pediatrics. 1987. 80:918–23. [Medline].
el-Shabrawi M, Wilkinson ML, Portmann B, et al. Primary sclerosing cholangitis in childhood. Gastroenterology. 1987. 92:1226-35. [Medline].
Debray D, Pariente D, Urvoas E, et al. Sclerosing cholangitis in children. J Pediatr. 1994. 124:49-56. [Medline].
Wilschanski M, Chait P, Wade JA, et al. Primary sclerosing cholangitis in 32 children: clinical, laboratory, and radiographic features, with survival analysis. Hepatology. 1995. 22:1415-22. [Medline].
Batres LA, Russo P, Mathews M, et al. Primary sclerosing cholangitis in children: a histologic follow-up study. Pediatr Dev Pathol. 2005. 8:568-76. [Medline].
Mendes FD, Lindor KD. Primary sclerosing cholangitis. Clin Liver Dis. 2004. 8:195-211. [Medline].
Ludwig J, Barham SS, LaRusso NF, Elveback LR, Wiesner RH, McCall JT. Morphologic features of chronic hepatitis associated with primary sclerosing cholangitis and chronic ulcerative colitis. Hepatology. 1981 Nov-Dec. 1(6):632-40. [Medline].
Kim WR, Therneau TM, Wiesner RH, et al. A revised natural history model for primary sclerosing cholangitis. Mayo Clin Proc. 2000 Jul. 75(7):688-94. [Medline].
Shetty K, Rybicki L, Carey WD. The Child-Pugh classification as a prognostic indicator for survival in primary sclerosing cholangitis. Hepatology. 1997 May. 25(5):1049-53. [Medline].
The Revised Natural History Model for Primary Sclerosing Cholangitis. Mayo Foundation for Medical Education and Research. Available at http://www.mayoclinic.org/gi-rst/mayomodel3.html. Accessed: March 30, 2012.
Kim WR, Poterucha JJ, Wiesner RH, et al. The relative role of the Child-Pugh classification and the Mayo natural history model in the assessment of survival in patients with primary sclerosing cholangitis. Hepatology. 1999 Jun. 29(6):1643-8. [Medline].
Bjornsson E, Angulo P. Cholangiocarcinoma in young indivuas with and without primary sclerosing cholangitis. Am J Gastroenterol. 2007. 102:1677-1682. [Medline].
Deneau M, Adler DG, Schwartz JJ, et al. Cholangiocarcinoma in a 17-year-old boy with primary sclerosing cholangitis and inflammatory bowel disease. J Pediatr Gastroenteorl Nutr. 2011. 52:617-620. [Medline].
Liu R, Cox K, Guthery SL, Book L, Witt B, Chadwick B, et al. Cholangiocarcinoma and High-Grade Dysplasia in Young Patients with Primary Sclerosing Cholangitis. Dig Dis Sci. 2014 Apr 19. [Epub ahead of print]:[Medline].
Miloh T, Arnon R, Shneider B, suchy F, Kerkar N. A retrospective Single-Center Review of Primary Sclerosing Cholangitis in Children. Clinical Gatroenterology and Hepatolog. 2009. 7:239-45. [Medline].
Miloh T, Anand R, Yin W, Vos M, Kerkar N, Alonso E. Pediatric liver transplantation for primary sclerosing cholangitis. Liver Transpl. 2011 Aug. 17(8):925-933. [Medline]. [Full Text].
Venkat VL, Ranganathan S, Mazariegos GV, Sun Q, Sindhi R. Recurrence of Primary Sclerosing Cholangitis in Pediatric Liver Transplant Recipients. Liver Transplantation. 2014 Jun. 20(6):679-86. [Medline].
Abu-Elmagd KM, Balan V. Recurrent primary sclerosing cholangitis: from an academic illusion to a clinical reality. Liver Transpl. 2005. 11:1326-8. [Medline].
Graziadei IW. Recurrence of primary sclerosing cholangitis after liver transplantation. Liver Transpl. 2002. 8:575-81. [Medline].
Shneider BL. Diagnostic and therapeutic challenges in pediatric primary sclerosing cholangitis. Liver Transpl. 2012 Mar. 18(3):277-81. [Medline].
Bangarulingam SY, Gossard AA, Petersen BT, Ott BJ, Lindor KD. Complications of endoscopic retrograde cholangiopancreatography in primary sclerosing cholangitis. Am J Gastroenterol. 2009 Apr. 104(4):855-60. [Medline].
Angulo P, Pearce DH, Johnson CD, et al. Magnetic resonance cholangiography in patients with biliary disease: its role in primary sclerosing cholangitis. J Hepatol. 2000 Oct. 33(4):520-7. [Medline].
Revelon G, Rashid A, Kawamoto S, Bluemke DA. Primary sclerosing cholangitis: MR imaging findings with pathologic correlation. AJR Am J Roentgenol. 1999 Oct. 173(4):1037-42. [Medline].
Fulcher AS, Turner MA, Franklin KJ, et al. Primary sclerosing cholangitis: evaluation with MR cholangiography—a case–control study. Radiology. 2000. 215:71-80. [Medline].
Ferrara C, Valeri G, Salvolini L, Giovagnoni A. Magnetic resonance cholangiopancreatography in primary sclerosing cholangitis in children. Pediatr Radiol. 2002. 32:413-17. [Medline].
Rustemovic N, Cukovic-Cavka S, Opacic M, Petrovecki M, Hrstic I, Radic D, et al. Endoscopic ultrasound elastography as a method for screening the patients with suspected primary sclerosing cholangitis. Eur J Gastroenterol Hepatol. 2009 Jun 2. [Medline].
Craig DA, MacCarty RL, Wiesner RH, et al. Primary sclerosing cholangitis: value of cholangiography in determining the prognosis. AJR Am J Roentgenol. 1991. 157:959-64. [Medline].
Olsson RG, Asztely MS. Prognostic value of cholangiography in primary sclerosing cholangitis. Eur J Gastroenterol Hepatol. 1995. 7:251-4. [Medline].
Ponsioen CY, Lam K, van Milligen de Wit AW, et al. Four years experience with short term stenting in primary sclerosing cholangitis. Am J Gastroenterol. 1999 Sep. 94(9):2403-7. [Medline].
Erickson NI, Balistereri WF. Sclerosing Cholangitis. S.R. Suchy FJ, Balistreri WF. Liver disease in children. 3. Cambridge University Press; 2007. 459-77.
Björnsson E. Management of primary sclerosing cholangitis. Minerva Gastroenterol Dietol. 2009 Jun. 55(2):163-72. [Medline].
Shi J, Li Z, Zeng X, Lin Y, Xie WF. Ursodeoxycholic acid in primary sclerosing cholangitis: meta-analysis of randomized controlled trials. Hepatol Res. 2009 May 7. [Medline].
Gilger MA, Gann ME, Opekun AR, Gleason WA Jr. Efficacy of ursodeoxycholic acid in the treatment of primary sclerosing cholangitis in children. J Pediatr Gastroenterol Nutr. 2000 Aug. 31(2):136-41. [Medline].
Pardi DS, Loftus EV, Kremers WK, et al. Ursodeoxycholic acid as a chemopreventive agent in patients with ulcerativecolitis and primary sclerosing cholangitis. Gastroenterology. 2003 Apr. 124(4):889-93. [Medline].
Tung BY, Emond MJ, Haggitt RC, et al. Ursodiol use is associated with lower prevalence of colonic neoplasia in patients with ulcerative colitis and primary sclerosing cholangitis. Ann Intern Med. 2001 Jan 16. 134(2):89-95. [Medline]. [Full Text].
Kochhar R, Goenka MK, Das K, Nagi B, Bhasin DK, Chawla YK, et al. Primary sclerosing cholangitis: an experience from India. J Gastroenterol Hepatol. 1996. 11(5):429. [Medline].
Angulo P, Batts KP, Jorgensen RA, LaRusso NA, Lindor KD. Oral budesonide in the treatment of primary sclerosing cholangitis. Am J Gastroenterol. 2000. 95(9):2333. [Medline].
Kyokane K, Ichihara T, Horisawa M, Suzuki N, Ichihara S, Suga S, et al. Successful treatment of primary sclerosing cholangitis with cyclosporine and corticosteroid. Hepatogastroenterology. 1994. 41(5):449. [Medline].
Van Thiel DH, Carroll P, Abu-Elmagd K, Rodriguez-Rilo H, Irish W, McMichael J, et al. Tacrolimus (FK 506), a treatment for primary sclerosing cholangitis: results of an open-label preliminary trial. Am J Gastroenterol. 1995. 90(3):455. [Medline].
Knox TA, Kaplan MM. Treatment of primary sclerosing cholangitis with oral methotrexate. Am J Gastroenterol. 1991. 86(5):546. [Medline].
Knox TA, Kaplan MM. A double-blind controlled trial of oral-pulse methotrexate therapy in the treatment of primary sclerosing cholangitis. Gastroenterology. 1994. 106(2):494. [Medline].
Davies YK, Cox KM, Abdullah BA, Safta A, Terry AB, Cox KL. Long-term treatment of primary sclerosing cholangitis in children with oral vancomycin: an immunomodulating antibiotic. J Pediatr Gastroenterol Nutr. 2008. 47(1):61. [Medline].
Tabibian JH, Weeding E, Jorgensen RA, Petz JL, Keach JC, Talwalkar JA, et al. Randomised clinical trial: vancomycin or metronidazole in patients with primary sclerosing cholangitis - a pilot study. Aliment Pharmacol Ther. March 2013. 37(6):604-12. [Medline].
Gow PJ, Chapman RW. Liver transplantation for primary sclerosing cholangitis. Liver. 2000 Apr. 20(2):97-103. [Medline].
Graziadei IW, Wiesner RH, Marotta PJ, et al. Long-term results of patients undergoing liver transplantation for primary sclerosing cholangitis. Hepatology. 1999 Nov. 30(5):1121-7. [Medline].
Liden H, Norrby J, Friman S, Olausson M. Liver transplantation for primary sclerosing cholangitis--a single- center experience. Transpl Int. 2000. 13 Suppl 1:S162-4. [Medline].
Sekido H, Takeda K, Morioka D, et al. Liver transplantation for primary sclerosing cholangitis. J Hepatobiliary Pancreat Surg. 1999. 6(4):373-6. [Medline].
Shimizu M, Iwasaki H, Mase S, Yachie A. Successful treatment of primary sclerosing cholangitis with a steroid and a probiotic. Case Rep Gastroenterol. 2012 May. 6(2):249-53. [Medline]. [Full Text].
Abdo AA, Bain VG, Kichian K, Lee SS. Evolution of autoimmune hepatitis to primary sclerosing cholangitis: A sequentialsyndrome. Hepatology. 2002 Dec. 36(6):1393-9. [Medline].
Angulo P, Larson DR, Therneau TM, et al. Time course of histological progression in primary sclerosing cholangitis. Am J Gastroenterol. 1999 Nov. 94(11):3310-3. [Medline].
Bambha K, Kim WR, Talwalkar J, et al. Incidence, clinical spectrum, and outcomes of primary sclerosing cholangitisin a United States community. Gastroenterology. 2003 Nov. 125(5):1364-9. [Medline].
Bergquist A, Glaumann H, Persson B, Broome U. Risk factors and clinical presentation of hepatobiliary carcinoma in patients with primary sclerosing cholangitis: a case-control study. Hepatology. 1998 Feb. 27(2):311-6. [Medline].
Bharucha AE, Jorgensen R, Lichtman SN, et al. A pilot study of pentoxifylline for the treatment of primary sclerosing cholangitis. Am J Gastroenterol. 2000 Sep. 95(9):2338-42. [Medline].
Boberg KM, Lundin KE, Schrumpf E. Etiology and pathogenesis in primary sclerosing cholangitis. Scand J Gastroenterol Suppl. 1994. 204:47-58. [Medline].
Chalasani N, Baluyut A, Ismail A, et al. Cholangiocarcinoma in patients with primary sclerosing cholangitis: a multicenter case-control study. Hepatology. 2000 Jan. 31(1):7-11. [Medline].
Floreani A, Rizzotto ER, Ferrara F, Carderi I, Caroli D, Blasone L. Clinical course and outcome of autoimmune hepatitis/primary sclerosing cholangitis overlap syndrome. Am J Gastroenterol. 2005 Jul. 100(7):1516-22. [Medline].
Harrison PM. Diagnosis of primary sclerosing cholangitis. J Hepatobiliary Pancreat Surg. 1999. 6(4):356-60. [Medline].
Kita R, Kita-Sasai Y, Hanaoka I, et al. Beneficial effect of bezafibrate on primary sclerosing cholangitis (three casereports). Am J Gastroenterol. 2002 Jul. 97(7):1849-51. [Medline].
Kugelmas M, Spiegelman P, Osgood MJ, et al. Different immunosuppressive regimens and recurrence of primary sclerosing cholangitisafter liver transplantation. Liver Transpl. 2003 Jul. 9(7):727-32. [Medline].
Lee YM, Kaplan MM. Medical treatment of primary sclerosing cholangitis. J Hepatobiliary Pancreat Surg. 1999. 6(4):361-5. [Medline].
[Guideline] Mahadevan U, Kane S. American gastroenterological association institute medical position statement on the use of gastrointestinal medications in pregnancy. Gastroenterology. 2006 Jul. 131(1):278-82. [Medline].
[Guideline] Murray KF, Carithers RL Jr. AASLD practice guidelines: Evaluation of the patient for liver transplantation. Hepatology. 2005 Jun. 41(6):1407-32. [Medline].
Nakanuma Y, Harada K, Katayanagi K, et al. Definition and pathology of primary sclerosing cholangitis. J Hepatobiliary Pancreat Surg. 1999. 6(4):333-42. [Medline].
Olsson R, Boberg KM, de Muckadell OS, et al. High-dose ursodeoxycholic acid in primary sclerosing cholangitis: a 5-year multicenter, randomized, controlled study. Gastroenterology. 2005. 129:1464-72. [Medline].
Raj V, Lichtenstein DR. Hepatobiliary manifestations of inflammatory bowel disease. Gastroenterol Clin North Am. 1999 Jun. 28(2):491-513. [Medline].
Roozendaal C, de Jong MA, van den Berg AP, et al. Clinical significance of anti-neutrophil cytoplasmic antibodies (ANCA) in autoimmune liver diseases. J Hepatol. 2000 May. 32(5):734-41. [Medline].
Saarinen S, Olerup O, Broome U. Increased frequency of autoimmune diseases in patients with primary sclerosing cholangitis. Am J Gastroenterol. 2000 Nov. 95(11):3195-9. [Medline].
Shetty K, Rybicki L, Brzezinski A, et al. The risk for cancer or dysplasia in ulcerative colitis patients with primary sclerosing cholangitis. Am J Gastroenterol. 1999 Jun. 94(6):1643-9. [Medline].
Talwalkar JA, Lindor KD. Primary sclerosing cholangitis. Inflamm Bowel Dis. 2005 Jan. 11(1):62-72. [Medline].