Pediatric Protein-Losing Enteropathy Follow-up

Updated: Jul 25, 2017
  • Author: Simon S Rabinowitz, MD, PhD, FAAP; Chief Editor: Carmen Cuffari, MD  more...
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Follow-up

Further Outpatient Care

All patients diagnosed with or at risk for protein-losing enteropathy (PLE) require regular evaluation for adequate growth and evidence of fat-soluble vitamin (ADEK) deficiencies.

Patients who develop PLE after Fontan procedures represent a particularly vulnerable cohort with a high rate of significant morbidity and mortality.

Close follow-up coupled with an aggressive approach to reverse this problem is warranted.

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Complications

Complications may include debilitating edema, failure to thrive, fat-soluble vitamin deficiencies.

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Prognosis

The most important variable is the underlying cause of the protein-losing enteropathy.

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Patient Education

Familiarize the patient and his or parents with the signs of edema and the earliest signs and symptoms of fat-soluble vitamin deficiency, and inform them that increased infections could be secondary to loss of immunoglobulins and/or lymphocytes. An ongoing relationship with the physician and frequent monitoring is essential to minimize morbidity.

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