Complications
See the list below:
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For complications of Klippel-Trenaunay-Weber syndrome, see Clinical.
Prognosis
See the list below:
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Recognition of the spectrum of severity is important, both in venous disease and in limb hypertrophy.
Jacob et al found that the rate of progression of limb length discrepancy was neither uniform nor predictable. [20] In Jacob et al's series, only 11% of patients had hypertrophy severe enough to warrant epiphysiodesis.
Amputation of an extremity is rarely necessary.
Patients with Klippel-Trenaunay syndrome (KTS) face a lifetime of potential problems, including cellulitis, lymph seepage, gangrene, skin breakdown, thrombophlebitis, and internal and superficial hemorrhage.
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Parkes Weber syndrome presents more severe problems, with hypertrophy, lymphedema, and cardiac hypertrophy. In one study by Robertson, 1 of 28 patients died from cardiac failure, and 5 of 28 required amputation of an extremity. [8]
Patient Education
See the list below:
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Information regarding the Klippel-Trenaunay Support Group is available online.
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Klippel-Trenaunay syndrome in a young person. Note the port-wine stain extending to the buttocks. These lesions can be associated with venous malformations involving the rectum and bladder.
