Pediatric Polycythemia Follow-up

Updated: Jun 13, 2023
  • Author: May C Chien, MD; Chief Editor: Lawrence C Wolfe, MD  more...
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Follow-up

Complications

The following are complications of polycythemia vera:

  • Vascular occlusive events - Splenic infarcts, thrombosis (cerebral, portal vein, pulmonary embolus)

  • Hemorrhage

  • Marrow fibrosis resulting in pancytopenia

  • Malignancy - Acute myelogenous leukemia (AML), chronic lymphocytic leukemia (CLL), chronic myelogenous leukemia (CML), lymphoma

  • Hyperuricemia - Renal stones, nephropathy, gout

  • Budd-Chiari syndrome