Pediatric Factor XIII Deficiency Follow-up

Updated: Mar 15, 2019
  • Author: Helge Dirk Hartung, MD; Chief Editor: Cameron K Tebbi, MD  more...
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Follow-up

Further Outpatient Care

Ideally, a comprehensive hemophilia care team with experience in the diagnosis and management of inherited bleeding disorders should monitor individuals with severe factor XIII (FXIII) deficiency.

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Deterrence/Prevention

For patients with homozygous factor XIII deficiency, prophylaxis is the best approach. [11]

  • Individuals who require plasma-derived factor XIII concentrate should be immunized with hepatitis A and hepatitis B vaccines.

  • Aspirin and other drugs that impair platelet function should be avoided.

  • Women at risk for spontaneous abortion should be evaluated for the need of enhanced prophylaxis starting in early pregnancy.

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Patient Education

Provide patients and families with individual instruction and educational materials so they can understand factor XIII deficiency, recognize the symptoms and signs of bleeding, and identify emergency situations.

  • Patients should know where to receive emergency care and how to contact their treatment center for immediate treatment.

  • Patients should wear a MedicAlert bracelet or carry other identification stating their bleeding disorder and recommended therapy.

For excellent patient education resources, visit eMedicineHealth's Oral Health Center. Also, see eMedicineHealth's patient education article Teething.

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